فیبروز کیستیک (سیستیک فیبروزیس) Cystic Fibrosis
- نوع فایل : کتاب
- زبان : انگلیسی
- نویسندگان : Marcus A. Mall, J. Stuart Elborn
- چاپ و سال / کشور: 2014
- تعداد صفحه : 342
Description
Cystic fibrosis (CF) is one of the most common fatal hereditary diseases. The discovery of the cystic fibrosis transmembrane conductance regulator (CFTR) gene 25 years ago set the stage for unraveling the pathogenesis of CF lung disease, continuous refinement of symptomatic treatments and the development of mutation-specific therapies, which are now becoming available for a subgroup of patients. This book provides an update on all aspects of CF lung disease, from infancy to adulthood, including current concepts on disease process, improvements in early diagnosis and monitoring, therapeutic approaches, and patient care. The book highlights important recent developments and discusses the next steps that will be required for further improvement of the life expectancy and quality of life of CF patients
