Conservative management of endolymphatic sac tumors in von Hippel–Lindau disease: case report
- نوع فایل : کتاب
- زبان : انگلیسی
- مؤلف : Matthieu Peyre & Stephan Gaillard & Remy van Effenterre & Sophie Giraud & Stéphane Richard
- چاپ و سال / کشور: 2010
Description
In endolymphatic sac tumors associated with von Hippel–Lindau disease, early detection and surgery have been warranted to avoid associated neurological morbidity. However, in lately discovered tumors, hearing preserving surgery is often impossible and timing of surgical resection is difficult to define. We report two cases of tumors revealed by a sudden and profound hearing loss and managed conservatively for more than 15 years without worsening of the neurological symptoms associated with the endolymphatic sac tumor. Tumor size remained stable for the first patient and a stuttering growth pattern was observed for the second patient. Initial observation may be considered a not unreasonable management paradigm in these cases.
Acta Neurochir (2011) 153:42–47 Received: 6 September 2010 / Accepted: 4 November 2010 / Published online: 20 November 2010
