Rosai-Dorfman disease mimicking mediastinal lymphoma
- نوع فایل : کتاب
- زبان : انگلیسی
- مؤلف : Kaoru Kaseda, MD · Hirotoshi Horio, MD Tsunekazu Hishima, MD · Tai Hato, MD Masahiko Harada, MD
- چاپ و سال / کشور: 2011
Description
Rosai-Dorfman disease is rare and typically presents with cervical lymphadenopathy. The disease is generally indolent and self-limited, but it carries a poor or fatal prognosis when it is advanced or when it involves and compresses vital structures. We herein report a rare case of Rosai-Dorfman disease affecting only the mediastinal- hilar region in a 66-year-old woman.
Gen Thorac Cardiovasc Surg (2011) 59:385–387 DOI 10.1007/s11748-010-0679-7 Received: 12 April 2010 / Accepted: 13 July 2010