Hydranencephaly associated with cerebellar involvement and bilateral microphthalmia and colobomas
- نوع فایل : کتاب
- زبان : انگلیسی
- مؤلف : Kishor B. Taori & Kiran M. Sargar & Amit Disawal & Shyam Chhadi & Jawahar Rathod
- چاپ و سال / کشور: 2010
Description
Hydranencephaly is an encephaloclastic central nervous system disorder characterised by severe destruction of the cerebral hemispheres with preservation of posterior fossa structures. We present MRI and neurosonography features of a unique case of hydranencephaly involving cerebellum (in the form of complete liquefaction of cerebellar hemispheres) and cerebral hemispheres with associated bilateral microphthalmia and ocular colobomas. This is an exceptional case as to the best to our knowledge. In humans, such a severe involvement of cerebellum has not been reported in cases of hydranencephaly. It is essential to distinguish hydranencephaly from gross hydrocephalus, as treatment and prognosis of the two are totally different. During differentiation, it is important to remember that severe cerebellar involvement can be seen in hydranencephaly.
Pediatr Radiol (2011) 41:270–273 DOI 10.1007/s00247-010-1749-9 Received: 27 March 2010 / Revised: 12 May 2010 / Accepted: 2 June 2010 / Published online: 25 June 2010
